Prof. MUDr. Jiří Zeman, DrSc. from 1st Faculty of Medicine receives Education Ministe ****************************************************************************************** * ****************************************************************************************** November 10, 2011, by: Lucie Kettnerová, Section: i-Forum informs On November 10, Prof. MUDr. Jiří Zeman, DrSc., from the 1st Faculty of Medicine received t the Minister of Education, Youth and Sport for outstanding results in research, experiment and innovations for 2011. The ceremony was held in the Great Mirror Hall of the ministry b laudatory speech was given by the Prorector for Doctoral Programmes and Academic Qualifica Ivan Jakubec, CSc. This year, the evaluation committee received 16 nominations and finally four honours. Besides Prof. J. Zeman, the other award-winners included Prof. RNDr. Julius Lukeš, CSc., f Centre of the Czech Academy of Science; Prof. RNDr. Emil Paleček, DrSc., from the Institut of the Czech Academy of Sciences; and Prof. RNDr. Radek Zbořil, PhD., from Palacký Univers Prof. MUDr. Jiří Zeman, DrSc. from the Department of Paediatrics and Adolescent Medicine o of Medicine and General Teaching Hospital in Prague. Professor Zeman graduated from the Charles University Pediatric Faculty in Prague and sinc at the Department of Paediatrics and Adolescent Medicine of the 1st Faculty of Medicine, i years as its head. In his research Prof. Zeman focuses on hereditary me 150 publications including a number of monographs; h reached 1152, his Hirsch index is 20. Along with his diseases and a gene for mucopolysaccharidosis type I scientific work, among them the Health Minister’s Aw editorial boards of both Czech and foreign scientifi Mitochondrial disorders of energy metabolism represe tissues with high energy consumption, mainly the bra exception in human biology, are controlled by two ge Prof. Zeman and his students in the “mitochondrial team” have significantly helped to incr the biological basis of several mitochondrial diseases and their impact on the affected ch Prof. Zeman and his team published five works in various journals with the overall impact The research had been carried out with support from the Ministry of Education, Youth and S University Grant Agency and the Internal Grant Agency of the Health Ministry. The team was the first to define a detailed clinical and laboratory phenotype in 25 childr mitochondrial encephalocardiomyopathy caused by a mutation in the TMEM70 gene. Laboratory by them serve as markers for the diagnosis of mitochondrial disorders in children. Prof. Zeman has for a long time systematically focused on research into mitochondrial diso with his colleagues he has prepared a number of cell lines and tissue specific models for mitochondrial biogenesis and mitochondrial functions in the prenatal and postnatal periods helping to improve understanding of the etiopathogenesis of mitochondrial diseases. One of significant scientific achievements is his contribution to the discoveries of several new diseases.